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NGS and MRD — Clinical Importance in AML

NGS and MRD — Clinical Importance in AML

Part I: Next-Generation Sequencing (NGS)

What NGS Does

NGS (next-generation sequencing) is a massively parallel DNA/RNA sequencing platform that can interrogate hundreds to thousands of genomic loci simultaneously from a single clinical sample. In AML workup, an NGS panel is run on bone marrow at diagnosis to:

  1. Identify somatic mutations — driver and cooperating lesions in the leukemic clone
  2. Classify the disease — WHO/ICC 2022 classification requires molecular data; morphology alone is insufficient
  3. Assign ELN risk — favorable / intermediate / adverse risk stratification is mutation-driven
  4. Guide therapy selection — targetable mutations (FLT3, IDH1/2, NPM1) dictate whether targeted agents are added; non-targetable mutations (ASXL1, SRSF2, TP53) confirm the need for HMA-based regimens
  5. Establish MRD targets — the diagnostic VAF of each mutation becomes the baseline for longitudinal monitoring

Ishamma's NGS (Oncomine Myeloid Assay GX V2)

Lab: Agilus Diagnostics, Gurugram | Sample date: 2025-11-22 | QC: 3345x coverage, 99.54% uniformity — high-quality run

Gene Change VAF Clinical Significance
RUNX1 p.(Asp93GlyfsTer32) 4% Adverse-risk AML per ELN/WHO 2022; preferred MRD target
ASXL1 p.(Trp1411Ter) 28% Epigenetic deregulator; inferior OS; confirms secondary-type AML; CHIP-prone
BCOR p.(Arg810Ter) 17% BCL6 corepressor LOF; founding/co-founding clone
SRSF2 p.(Pro95His) 31% Canonical CHIP hotspot; splicing dysregulation; adverse prognostic
STAG2 p.(Met1102TyrfsTer34) 16% Cohesin LOF; genomic instability; X-linked
NRAS p.(Gly12Asp) 3% Subclonal MAPK activator; unstable — not suitable for MRD

RNA fusion panel: Negative — no gene rearrangements detected.

Net diagnostic output from NGS:
- Classified as AML with myelodysplasia-related gene mutations (WHO/ICC 2022) — requires multiple MDS-related gene mutations, which Ishamma has (ASXL1, BCOR, SRSF2, STAG2)
- Adverse ELN risk — driven by RUNX1 + ASXL1 + SRSF2
- No targetable mutations (no FLT3-ITD/TKD, no IDH1/2, no NPM1) — confirms Aza-Ven as the appropriate backbone
- Provides the mutation inventory from which MRD targets are selected


Part II: Measurable Residual Disease (MRD)

What MRD Is

MRD is the detection of residual leukemic cells below the threshold of conventional morphology (<5% blast threshold by microscopy) or standard cytogenetics. High-sensitivity assays — including NGS, digital PCR (dPCR), and multiparameter flow cytometry (MFC) — can detect 1 leukemic cell in 10,000–1,000,000 normal cells (10⁻⁴ to 10⁻⁶ sensitivity).

Why MRD Matters

Scenario Implication
Morphologic CR, MRD-negative Deepest achievable response; best prognosis; supports dose de-escalation or cycle spacing
Morphologic CR, MRD-positive Residual disease persists; 2–4× higher relapse risk; warrants closer monitoring or therapy intensification
MRD rising (previously negative) Molecular relapse — precedes overt blast relapse by weeks to months; enables preemptive regimen change
MRD stable (persistent low positive) Clone present but controlled; watch-and-wait vs. therapy adjustment depends on trajectory

NGS as MRD Platform

NGS-based MRD tracking re-sequences the same loci identified at diagnosis, measuring whether the VAF of each mutation has fallen (response), is undetectable (remission), or is rising (relapse). Compared to PCR, NGS-MRD is:
- Broader — can track multiple mutations simultaneously (composite panel)
- Mutation-agnostic — does not require a pre-designed probe per mutation (as PCR does)
- Sensitive at ≥0.1–1% VAF with high-depth sequencing (error-corrected NGS approaches reach 0.01%)


Part III: NGS → MRD Continuum in Ishamma's Case

Step 1 — Diagnostic NGS (Nov 2025)

The Oncomine panel identified the 6-mutation clonal architecture. This step is done.

Step 2 — Select MRD Targets

Not all mutations are equal as MRD markers (see Mrd Targets Explained for full rationale):

Mutation MRD Role Reason
RUNX1 Primary target Frameshift — leukemia-specific, not CHIP-associated, Tier I
STAG2 Supplementary Less CHIP-prone than ASXL1/SRSF2; supports composite assessment
BCOR Supplementary Co-founding clone; low VAF persistence may reflect residual CHIP
ASXL1, SRSF2 Not solo targets Canonical CHIP mutations — persist even after leukemia eradication
NRAS Excluded Subclonal, unstable — not trackable

Recommended composite panel: RUNX1 primary + BCOR + STAG2. All three undetectable = high-confidence MRD-negative.

Step 3 — Serial MRD Monitoring

No molecular MRD testing has been performed to date.

The Day 21 BMBx (Bone Marrow Biopsy 2025 12 31) confirmed morphologic response (cellularity 60% → 25–30%), but morphology cannot determine whether the leukemic clone is contracting at a molecular level.

Standard NGS-MRD cadence on Aza-Ven for non-transplant AML:
- After Cycle 2–3: First molecular assessment — establishes whether RUNX1 VAF has cleared or persists
- After Cycle 4–6: Second assessment — confirms trajectory (deepening response vs. plateau)
- Every 3–6 months thereafter: Ongoing surveillance; key decision point at each cycle reassessment

Why MRD Monitoring Matters Even Without Transplant Eligibility

At 81 years, allo-HSCT is not feasible. MRD monitoring still serves 4 non-transplant functions:

  1. Treatment duration — MRD-negative on Aza-Ven supports considering cycle spacing or dose de-escalation to reduce cumulative cytopenias and improve QoL
  2. Dose justification — VEN has already been reduced (10d → 5d) and AZA capped at 5d. MRD data provides objective justification for further reductions vs. requiring intensification
  3. Early relapse detection — RUNX1 VAF rise will precede blast relapse on CBC/morphology by weeks to months; intervention is more effective before overt relapse
  4. Distinguishing CHIP from active disease — At 81, ASXL1 (28%) and SRSF2 (31%) will likely persist in bone marrow indefinitely regardless of leukemia control; RUNX1 clearance is the clean signal for true remission

Current Status Summary

Parameter Status
Diagnostic NGS Done (Nov 2025, Oncomine — high quality)
Morphologic response Confirmed (Day 21 BMBx, Dec 2025)
MRD target defined RUNX1 (primary), per Agilus recommendation
NGS-MRD post-treatment Not done — critical gap
Recommended timing After Cycle 2–3 (was Feb–Mar 2026; now overdue at Cycle 4+)
MRD gap is now post-Cycle 4

NGS-MRD with RUNX1 VAF tracking is overdue. Recommend raising with Bijay Prabhakaran Nair at next visit. Test can be performed from peripheral blood (liquid biopsy) or bone marrow aspirate. Lab: Agilus Diagnostics (same lab that ran the diagnostic panel — ensures assay continuity).


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Filed from query, 2026-05-03.